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| CASE REPORT |
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| Year : 2006 |
Volume
: 17 | Issue : 1 | Page
: 50-53 |
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Nevoid basal cell carcinoma syndrome
Karthiga S Kannan1, Sivapatha B Sundharam2, R Manikandan3
1 Department of Oral Medicine & Radiology, Sree Mookambika Institute of Dental Sciences, V.P.M. Hospital Complex, Padanilam, Kulasekharam-629 161, India
2 Department of Oral and Maxillofacial Pathology, Meenakshi Ammal Dental College and Hospial, Madhuravoyal, Chennai-602 102, India
3 Department of Oral and Maxillofacial Surgery, Meenakshi Ammal Dental College and Hospial, Madhuravoyal, Chennai-602 102, India
Correspondence Address:
Karthiga S Kannan
Department of Oral Medicine & Radiology, Sree Mookambika Institute of Dental Sciences, Padanilam, Kulasekharam-629 161
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0970-9290.29891
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Binkley and Johnson first reported this syndrome in 1951. But it was in 1960, Gorlin-Goltz established the association of basal cell epithelioma, jaw cyst and bifid ribs, a combination which is now frequently known as Gorlin-Goltz syndrome as well as Nevoid Basal Cell Carcinoma Syndrome (NBCCS). NBCCS is inherited as an autosomal dominant trait with high penetrance and variable expressivity. NBCCS is characterized by variety of cutaneous, dental, osseous, opthalmic, neurologic and sexual abnormalities. One such case of Gorlin-Goltz syndrome is reported here with good illustrations. |
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